MEDICAL FORMULAS FOR UCDs
- Vitaflo
- Abbott Metabolic
- Nutricia
- Mead/Johnson
- WND 1 Important: Supply Disruptions
MEDICATIONS AND SUPPLEMENTS FOR UCDs
Amgen Therapeutics
Ravicti® (phenylbutyrate in a glycerol liquid) for treatment of UCD
Buphenyl® powder or capsules (sodium phenylbutyrate) for treatment of UCD
Zevra Therapeutics
Olpruva® (sodium phenylbutyrate) oral suspension for treatment of UCD
Lucane Pharma
Pheburane® granules (coated pellets, tasteless sodium phenylbutyrate) for treatment of UCD
SigmaPharm
CITRULLINE AND ARGININE
Note: only pharmaceutical grade citrulline and arginine are recommended for use in Urea Cycle Disorders. Over-the-counter products can be of questionable potency, containing fillers, and quality and are not recommended. Underdosing could result.
Montiff Inc. - Suppliers of pharmaceutical grade L-citrulline and L-arginine. (Gives discount to NUCDF families)
3205 Santa Monica Blvd.
Los Angeles, CA 90025
Phone: (877)820-4883 Fax: (310) 582-8939
www.montiff.com
Vitaflo - Suppliers of pharmaceutical-grade amino acid supplements (available by prescription)
Jo Mar Labs - Suppliers of pharmaceutical grade L-citrulline and L-arginine.
WARNING:
Feb 14, 2014 FDA DRUG RECALL - CITRULLINE:
L-citrulline manufactured by Medisca, a supplier to hospitals and pharmacies, was recalled. Lots 95482/A, 95482/B, 95482/C, 95482/D &96453/A, 96453/B, 96453/C, 96453/D contained ZERO citrulline. The product contained a different amino acid, L-acetyl-leucine. This resulted in reports of severe side effects including metabolic instability, hyperammonemia, hair loss, stomach pains and other symptoms. The FDA issued a warning and manufacturer recall HERE. Adverse events should be reported on FDA MedWatch HERE. Please notify your pharmacy and your metabolic physician immediately if you notice a change or difference in the usual color, consistency, or odor of UCD treatment amino acid supplements. The amino acid supplements can be tested for purity to ensure that the product contains the labeled quality/strength. If you suspect an issue with your citrulline or arginine, contact NUCDF for more information on how to get the product tested.
Disclaimer: Information is provided for reference only and does not constitute an endorsement of any product or manufacturer by NUCDF.
Smiles from our 2011 NUCDF Conference
We are very happy to be in contact with NUCDF for the support and answers to our questions relating to this disorder. If it was not for this organization, there wouldn’t be anywhere for families like ours to turn for support and questions relating to UCDs. C.B.
